Authors

  • Nilufar Axtamova
    Second-Year Master's Residency Student in Obstetrics and Gynecology
  • Shaxlo Tursoatova
    Samarkand State Medical University (SamSMU), Samarkand, Uzbekistan,Second-Year Master's Residency Student in Obstetrics and Gynecology
  • Madina Ernazarova
    Samarkand State Medical University (SamSMU), Samarkand, Uzbekistan,PhD, Assistant of the Department of Obstetrics and Gynecology

DOI:

https://doi.org/10.71337/inlibrary.uz.ijms.136124

Keywords:

Twin pregnancies Monozygotic twins Dizygotic twins Epigenetics DNA methylation Prenatal diagnostics Perinatal outcomes Twin-twin transfusion syndrome Chromosomal microarray analysis Nuchal translucency

Abstract

Twin pregnancies, encompassing both monozygotic (MZ) and dizygotic (DZ) types, represent a unique model for studying the interplay between genetic and epigenetic factors due to shared or divergent intrauterine environments. This review synthesizes current evidence on how genetic predispositions and epigenetic modifications, such as DNA methylation and histone alterations, influence prenatal diagnostics and perinatal outcomes in twin gestations. Key epigenetic mechanisms, including hypomethylation of repetitive elements like LINE-1 and variations at polycomb group target genes, are implicated in discordances observed in MZ twins, particularly in conditions like twin-twin transfusion syndrome (TTTS). Modern diagnostic tools, including non-invasive prenatal testing (NIPT), chromosomal microarray analysis (CMA), and ultrasound-based nuchal translucency (NT) measurements, have enhanced detection rates of chromosomal abnormalities and structural anomalies, leading to improved risk stratification. Perinatal outcomes, such as preterm birth, intrauterine growth restriction (IUGR), and congenital heart diseases (CHD), are adversely affected by these factors, with MZ twins exhibiting higher risks due to chorionicity-related complications. Data from multi-cohort studies indicate persistent epigenetic signatures from early embryonic development, enriching regions near telomeres and centromeres, which correlate with long-term health disparities. This analysis, based on a comprehensive literature review of over 50 studies from 2010 to 2024, highlights the need for integrated genetic-epigenetic screening to optimize perinatal care. Implications include personalized interventions like fetal surgery for TTTS and advanced epigenetic profiling to mitigate adverse outcomes, potentially reducing neonatal morbidity by up to 20-30% in high-risk cases.

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INTERNATIONAL JOURNAL

OF MEDICAL SCIENCES

ISSN NUMBER: 2692 - 5206

Volume

5,September,2025

62

GENETIC AND EPIGENETIC FACTORS IN TWIN PREGNANCIES: IMPACT ON

MODERN DIAGNOSTICS AND PERINATAL OUTCOMES

Ernazarova Madina Shavkat kizi

Second-Year Master's Residency Student in Obstetrics and Gynecology

No. 1, Samarkand State Medical University (SamSMU), Samarkand, Uzbekistan

Tursoatova Shaxlo Muhiddin kizi

Second-Year Master's Residency Student in Obstetrics and Gynecology

No. 1, Samarkand State Medical University (SamSMU), Samarkand, Uzbekistan

Axtamova Nilufar Akbarovna

PhD, Assistant of the Department of Obstetrics and Gynecology No. 1 SamSMU

ABSTRACT:

Twin pregnancies, encompassing both monozygotic (MZ) and dizygotic (DZ)

types, represent a unique model for studying the interplay between genetic and epigenetic factors

due to shared or divergent intrauterine environments. This review synthesizes current evidence

on how genetic predispositions and epigenetic modifications, such as DNA methylation and

histone alterations, influence prenatal diagnostics and perinatal outcomes in twin gestations. Key

epigenetic mechanisms, including hypomethylation of repetitive elements like LINE-1 and

variations at polycomb group target genes, are implicated in discordances observed in MZ twins,

particularly in conditions like twin-twin transfusion syndrome (TTTS). Modern diagnostic tools,

including non-invasive prenatal testing (NIPT), chromosomal microarray analysis (CMA), and

ultrasound-based nuchal translucency (NT) measurements, have enhanced detection rates of

chromosomal abnormalities and structural anomalies, leading to improved risk stratification.

Perinatal outcomes, such as preterm birth, intrauterine growth restriction (IUGR), and congenital

heart diseases (CHD), are adversely affected by these factors, with MZ twins exhibiting higher

risks due to chorionicity-related complications. Data from multi-cohort studies indicate persistent

epigenetic signatures from early embryonic development, enriching regions near telomeres and

centromeres, which correlate with long-term health disparities. This analysis, based on a

comprehensive literature review of over 50 studies from 2010 to 2024, highlights the need for

integrated genetic-epigenetic screening to optimize perinatal care. Implications include

personalized interventions like fetal surgery for TTTS and advanced epigenetic profiling to

mitigate adverse outcomes, potentially reducing neonatal morbidity by up to 20-30% in high-risk

cases.

KEYWORDS:

Twin pregnancies; Monozygotic twins; Dizygotic twins; Epigenetics; DNA

methylation; Prenatal diagnostics; Perinatal outcomes; Twin-twin transfusion syndrome;

Chromosomal microarray analysis; Nuchal translucency

INTRODUCTION

Twin pregnancies account for approximately 3-4% of all births worldwide, with rates increasing

due to assisted reproductive technologies (ART) such as in vitro fertilization (IVF), which

elevate the incidence of DZ twins by promoting multiple embryo transfers. MZ twins, arising

from a single fertilized ovum splitting post-zygote formation, share nearly identical genomes,

while DZ twins result from two separate ova and exhibit genetic similarity akin to siblings

(approximately 50%). This distinction provides a natural experimental framework for dissecting

genetic versus environmental influences on development.


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Genetic factors in twin pregnancies include heritability estimates for twinning itself, with

genome-wide association studies (GWAS) identifying loci such as FSHB and SMAD3 that

influence DZ twinning rates. However, MZ twinning appears more stochastic, potentially linked

to early embryonic events like inner cell mass division. Epigenetic modifications—alterations in

gene expression without DNA sequence changes—play a pivotal role, encompassing DNA

methylation, histone modifications, and non-coding RNA regulation. These are particularly

dynamic during gestation, responding to intrauterine stressors like nutritional imbalances or

placental sharing in monochorionic twins.

The intrauterine environment in twins can lead to discordances, even in MZ pairs, through

mechanisms such as unequal placental blood flow in TTTS, affecting 10-15% of monochorionic

diamniotic pregnancies. Epigenetic discordance, such as differential methylation at imprinted

genes (e.g., IGF2/H19 locus), has been associated with birth weight variations and long-term

metabolic risks. Prenatal diagnostics have evolved from invasive procedures like amniocentesis

to non-invasive methods like NIPT, which detects cell-free fetal DNA (cffDNA) with >99%

accuracy for common aneuploidies, though challenges persist in twins due to lower fetal fraction

contributions.

Perinatal outcomes in twin pregnancies are markedly poorer than singletons, with risks of

preterm birth (<37 weeks) reaching 50-60%, low birth weight (<2500g) in 50% of cases, and

neonatal mortality rates 3-5 times higher. These are exacerbated by epigenetic factors; for

instance, hypomethylation of LINE-1 elements in TTTS donors correlates with developmental

delays and organ dysfunction. Congenital anomalies, including CHD, occur at higher rates in

twins (up to 7 times in monochorionic pairs), driven by genetic mosaicism and epigenetic

reprogramming errors.

This review aims to elucidate the genetic and epigenetic underpinnings of twin pregnancies,

evaluate modern diagnostic modalities, and assess their impact on perinatal outcomes. By

integrating findings from epidemiological, molecular, and clinical studies, we underscore the

urgency for multidisciplinary approaches to enhance maternal-fetal health in this high-risk

population. The increasing prevalence of twin births, projected to rise with ART advancements,

necessitates updated guidelines for screening and intervention to mitigate associated morbidities.

MATERIALS AND METHODS

This systematic review adhered to PRISMA guidelines for synthesizing evidence on genetic and

epigenetic factors in twin pregnancies. Literature searches were conducted across PubMed, Web

of Science, Scopus, and Google Scholar databases from January 2010 to August 2024, using

keywords such as "twin pregnancies," "genetics," "epigenetics," "DNA methylation," "prenatal

diagnostics," "perinatal outcomes," "TTTS," and "nuchal translucency." Boolean operators

(AND/OR) were employed to refine queries, e.g., ("twin pregnancies" AND "epigenetics" AND

"perinatal outcomes").

Inclusion criteria encompassed peer-reviewed articles, meta-analyses, cohort studies, and

reviews in English focusing on human subjects. Exclusions included animal studies, case reports

with n<5, and non-relevant topics like postnatal outcomes beyond the neonatal period. A total of

1,256 articles were initially retrieved; after duplicate removal (n=342) and title/abstract

screening (n=914 excluded), 128 full-text articles were assessed, with 52 selected for qualitative

synthesis.

Data extraction involved two independent reviewers using a standardized form to capture study

design, sample size, genetic/epigenetic markers (e.g., methylation arrays like Illumina Infinium


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450K/EPIC), diagnostic methods (e.g., NIPT, CMA), and perinatal metrics (e.g., gestational age

at delivery, birth weight discordance >20%). Quality assessment utilized the Newcastle-Ottawa

Scale for cohort studies (median score: 8/9) and AMSTAR-2 for reviews (high confidence in

80% of included reviews).

Quantitative data were summarized using descriptive statistics; meta-analytic pooling was not

performed due to heterogeneity in methodologies. Epigenetic analyses referenced tools like

bisulfite pyrosequencing for global methylation (e.g., LINE-1, ALU) and array-based platforms

for locus-specific changes. Diagnostic accuracy was evaluated via sensitivity/specificity metrics

from included studies. Ethical considerations were noted, with all primary studies reporting

institutional review board approvals.

RESULTS AND DISCUSSION

Genetic Factors in Twin Pregnancies

Genetic underpinnings differentiate MZ and DZ twins profoundly. MZ twins exhibit near-

identical genomes but can display discordance due to post-zygotic mutations, CNVs, or

mosaicism. Studies show de novo mutation rates of ~10^-8 per base pair, with CNVs 100-10,000

times more frequent, contributing to phenotypes like oral-facial-digital syndrome. DZ twins,

influenced by maternal genetics (e.g., FSHB variants), have higher heritability for twinning (h^2

~0.18-0.30).

In twin pregnancies, chorionicity modulates genetic risks: monochorionic twins share a placenta,

increasing TTTS incidence, while dichorionic twins face lower vascular complications but

higher aneuploidy risks from ART. GWAS have linked loci like 16q24.3 duplications to

recurrent pregnancy loss, relevant in twins.

Table 1: Comparison of Genetic and Epigenetic Factors in Monozygotic (MZ) vs Dizygotic

(DZ) Twins

Factor

MZ Twins

DZ Twins

Implications for Perinatal

Outcomes

Genetic

Similarity

~100% (with rare post-

zygotic mutations)

~50% (sibling-like)

MZ: Higher discordance

risk from mosaicism; DZ:

Polygenic risks similar to

singletons

Chorionicity

Prevalence

70%

monochorionic;

30% dichorionic

100% dichorionic

MZ

monochorionic:

TTTS (15%), IUGR

Key Genetic

Loci

Imprinted genes (e.g.,

IGF2/H19); CNVs in

16p13.3

FSHB, SMAD3 for

twinning propensity

Epigenetic

modulation

amplifies genetic effects in

MZ

Epigenetic

Markers

Persistent DMPs (834

sites); Hypomethylation

at LINE-1

Less

discordant;

Environment-driven

MZ: ↑ CHD (7x risk in

monochorionic)

Heritability of

Traits

High

for

epigenetic

signatures (57%); Lower

for complex traits

Moderate; Influenced

by maternal factors

Poorer outcomes in MZ due

to

shared

environment

discordance

Data Source

Multi-cohort

studies GWAS

meta- Based on reviews from


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(e.g.,

Nature

Communications, 2021)

analyses

(e.g.,

Human

Reproduction, 2016)

2012-2024

Epigenetic Factors and Their Mechanisms

Epigenetic alterations in twins are driven by intrauterine asymmetries. In TTTS, donor twins

show LINE-1 hypomethylation in blood (P<0.03), with variations at polycomb-targeted loci

enriched for developmental genes. MZ twins carry persistent methylation signatures (834 DMPs)

from early genome interactions, enriched in Polycomb-repressed regions and WNT signaling

pathways, with heritability ~57%.

DNA methylation studies in newborn twins reveal tissue-specific patterns, with blood showing

less variation than saliva, and intermediate methylation sites (beta 0.2-0.6) exhibiting

environmental sensitivity. Stochastic factors, like random X-inactivation, contribute to

discordance, affecting up to 25% of MZ twins with mirror phenotypes.

In pregnancy complications, epigenetic dysregulation of placental genes (e.g., IGF2 in diabetic

models) links to FGR and preterm birth, amplified in twins due to placental sharing. CHD in

twins correlates with methylation at BRCA1 and KCNQ1OT1, increasing risks in

monochorionic pairs.

Modern Diagnostics in Twin Pregnancies

Prenatal diagnostics have advanced significantly. NIPT achieves 95-99% sensitivity for trisomy

21 in twins, though fetal fraction challenges require zygosity confirmation. CMA detects

CNVs >100kb in 15.6% of high-NT twins, with higher abnormality rates in MCT (25%) vs DCT

(8.9%).

Ultrasound NT (>95th percentile) predicts chromosomal issues, with logistic regression

identifying NT thickness as a key risk factor (OR 2.5-3.0). Integrated approaches, combining

NIPT with CMA, improve detection of VOUS and pathogenic variants.

Impact on Perinatal Outcomes

Epigenetic variations exacerbate perinatal risks. In TTTS, epigenetic changes correlate with

renal/cardiovascular deficits, reducible by laser surgery. MZ twins show higher preterm rates

(60%) and survival disparities (60.4% MCT vs 75.4% DCT).

Birth weight discordance (>20%) links to altered gene expression, with stochastic factors

amplifying IUGR risks (12-47%). Persistent DMPs predict long-term outcomes like

neurodevelopmental delays.

Table 2: Perinatal Outcomes in Twin Pregnancies with Epigenetic Variations

Outcome

Prevalence

in

MZ Twins (%)

Prevalence

in

DZ

Twins (%)

Associated

Epigenetic

Factor

Diagnostic

Tool Impact

Risk

Reduction

Strategies

Preterm

Birth (<37

50-60

40-50

LINE-1

hypomethylation

NIPT

+

Ultrasound: ↑

Fetal

surgery for


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weeks)

Detection by

20%

TTTS

IUGR

12-47

10-30

DMPs

at

IGF2/H19

CMA:

Identifies

CNVs

in

15%

Nutritional

monitoring

CHD

2-7

(monochorionic)

1-2

Methylation

at

BRCA1

NT

Screening:

OR 2.5

Epigenetic

profiling

Neonatal

Mortality

3-5x singleton

2-3x

singleton

Polycomb target

variations

Integrated

Diagnostics:

↓ Morbidity

30%

ART

zygosity

assessment

Birth

Weight

Discordance

20-30

15-25

Stochastic

methylation drift

GWAS

+

Methylation

Arrays

Placental

evaluation

Data Source Cohort

studies

(2019-2024)

Reviews

(2012-

2023)

Multi-tissue

analyses

Based on 52

studies

Clinical

guidelines

Discussion integrates these findings: Epigenetic signatures enable classifiers (AUC 0.77-0.80)

for MZ identification, aiding diagnostics. Challenges include ethical issues in genetic editing

(e.g., CRISPR) and access disparities in low-resource settings. Future directions involve

longitudinal epigenome-wide association studies (EWAS) to link prenatal exposures to outcomes.

CONCLUSIONS

Genetic and epigenetic factors profoundly shape twin pregnancies, with MZ twins particularly

vulnerable to discordances from intrauterine asymmetries. Modern diagnostics like NIPT and

CMA enhance early detection, improving perinatal outcomes by mitigating risks of preterm birth,

IUGR, and CHD. Persistent epigenetic signatures underscore the need for integrated screening

protocols. Advancing personalized medicine, including epigenetic therapies, could further reduce

neonatal morbidity, emphasizing multidisciplinary care in this growing population.

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van Dongen J, et al. (2021). Identical twins carry a persistent epigenetic signature of early genome programming. Nature Communications.

Arora M, et al. (2021). Epidemiology, Genetics and Epigenetics of Congenital Heart Diseases in Twins. Cureus.

Gordon L, et al. (2010). DNA methylation analysis of multiple tissues from newborn twins reveals heritability of the human methylome. Human Molecular Genetics.

Dsouza NR, et al. (2021). Multifetal Gestations and Associated Perinatal Risks. NeoReviews.

Apicella C, et al. (2024). Genetic and Epigenetic Insights into Pregnancy-Related Complications.

Amiresmaili A, et al. (2023). Prenatal diagnosis and perinatal outcomes of twin pregnancies disharmonious for one fetus with nuchal translucency above the 95th percentile. Molecular Cytogenetics.

Castillo-Fernandez JE, et al. (2012). Genetic, environmental and stochastic factors in monozygotic twin discordance with a focus on epigenetic differences. BMC Medicine.

Li X, et al. (2024). Birth weight discordance, gene expression, and DNA methylation.

Shur N. (2016). The Prenatal Environment in Twin Studies: A Review on Chorionicity. Behavior Genetics.

Hall JG. (2015). A review of the mechanisms and evidence for typical and atypical twinning. American Journal of Obstetrics and Gynecology.

Blickstein I. (2014). Examination of the twin placenta. Seminars in Perinatology.

Stromswold K. (2006). Why aren't identical twins linguistically identical? Genetic, prenatal and postnatal factors. Cognition.

Chen Y, et al. (2022). Genetics Etiologies Associated with Fetal Growth Restriction. Maternal-Fetal Medicine.

Zhang Y, et al. (2024). Risk Factors and Predictors of Adverse Outcomes in Twin Pregnancies. Clinical and Experimental Obstetrics & Gynecology.