Authors

  • Shakhzoda Odilova
    Samarkand State Medical University
  • Aziza Tilavova
    Samarkand State Medical University

DOI:

https://doi.org/10.71337/inlibrary.uz.ijms.71610

Abstract

Congenital heart defects (CHDs) represent one of the most significant challenges in pediatric cardiology and cardiovascular surgery worldwide [1]. According to the World Health Organization (WHO), the incidence of CHDs ranges from 8 to 12 per 1,000 live births [2]. In the structure of childhood mortality, cardiovascular pathology remains one of the leading causes, with CHDs accounting for 30–45% of all mortality associated with congenital developmental anomalies [3].

 

 

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CONGENITAL HEART DEFECTS IN CHILDREN (LITERATURE REVIEW)

Odilova Shakhzoda Rustamovna

1st-year master's resident of the Department of Pediatrics and Neonatology, Samarkand

State Medical University, Samarkand, Uzbekistan.

Tilavova Aziza Komilovna

1st-year master's resident of the Department of Pediatrics and Neonatology, Samarkand

State Medical University, Samarkand, Uzbekistan.

Congenital heart defects (CHDs) represent one of the most significant challenges in pediatric

cardiology and cardiovascular surgery worldwide [1]. According to the World Health

Organization (WHO), the incidence of CHDs ranges from 8 to 12 per 1,000 live births [2].

In the structure of childhood mortality, cardiovascular pathology remains one of the leading

causes, with CHDs accounting for 30–45% of all mortality associated with congenital

developmental anomalies [3].

The formation of the heart in the fetus occurs during the earliest stages of embryogenesis,

when the basic structures of future organs and systems are being laid down [5]. External and

internal factors, such as genetic mutations, infectious agents, toxic exposures, and metabolic

disorders in the mother, can influence the process of heart and major vessel formation,

leading to various developmental defects [6]. Additionally, several studies highlight the

significant role of chromosomal abnormalities and syndromes in which the incidence of

CHDs is significantly higher than in the general population (e.g., Down syndrome or

DiGeorge syndrome) [7].

Modern methods of prenatal diagnosis, particularly fetal echocardiography, allow for the

detection of some defects as early as 18–20 weeks of gestation [8]. However, not all changes

in the cardiovascular system can be visualized prenatally, especially in cases of minor

defects or defects with mixed hemodynamics [9]. Timely diagnosis is critical for

determining the management strategy for the newborn (e.g., the need for emergency surgical

intervention or transfer to a specialized hospital) and reducing the risk of adverse outcomes

[10].

According to leading Russian clinics, there has been a relative decrease in severe forms of

CHDs in recent years due to the wider use of early ultrasound screening during pregnancy

[4]. However, some authors emphasize that in many regions, the level of specialized care for

expectant mothers remains insufficient, access to high-precision diagnostic equipment is

limited, and extended screening for chromosomal and genetic abnormalities is not routinely

performed [11]. As a result, children with CHDs do not always receive timely and accurate

diagnosis and treatment, which negatively affects survival rates and quality of life [12].

Significant interest lies in research on the structural classification of congenital heart defects,

which reflects the complexity and variability of defects in both morphological and

hemodynamic terms [13]. The most common forms include ventricular septal defects (VSD),

patent ductus arteriosus (PDA), atrial septal defects (ASD), tetralogy of Fallot, transposition


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of the great arteries (TGA), coarctation of the aorta, and others [14]. Critical CHDs requiring

urgent surgical intervention in the neonatal period (e.g., hypoplastic left heart syndrome) are

less common but have extremely high mortality rates in the absence of timely surgery [15].

According to several Russian authors, risk factors for CHDs include an unfavorable obstetric

and gynecological history (infections during pregnancy, use of teratogenic medications),

maternal age (over 35 years), environmental factors (air pollution, radiation), and hereditary

predisposition [16]. The polyetiological nature of CHDs is emphasized: often, multiple

causal factors may contribute to the formation of a single defect [17].

In pediatric practice, clinical symptoms play a crucial role, directly depending on the type

and severity of the defect and the degree of hemodynamic impairment [18]. In some children,

the defect may manifest immediately after birth (cyanosis, dyspnea, heart failure), while in

others, symptoms may appear later in childhood (episodes of weakness, fatigue, delayed

physical development) [19]. Diagnosis of CHDs, in addition to standard methods (physical

examination, electrocardiography, chest X-ray), includes echocardiography, Doppler

ultrasound, and often cardiac catheterization and angiocardiography [20]. Modern treatment

approaches are based on interventional cardiology and cardiac surgery, with the timing and

method of intervention depending on the morphology of the defect and the child's overall

condition [21].

One of the most pressing issues remains the determination of prognostic factors for

outcomes, particularly long-term survival, quality of life, and physical and psychomotor

development in children with CHDs [22]. Several large multicenter studies show that with

timely and adequate surgical treatment, many children can achieve satisfactory or even

normal health levels [23]. However, the presence of severe associated developmental defects

(including those outside the cardiovascular system), genetic syndromes, and other

complicating factors can significantly worsen the prognosis [24].

Thus, the analysis of scientific literature indicates the high prevalence of congenital heart

defects and their significant impact on childhood morbidity and mortality rates. Despite

advances in modern diagnosis and treatment, challenges remain in early detection,

preoperative preparation, and rehabilitation of children with CHDs, as well as in prevention

and genetic counseling [25]. This article provides a literature review aimed at systematizing

current knowledge on congenital heart defects in children, from epidemiology and

classification to diagnostic and therapeutic approaches.

**Brief Overview of Epidemiology and Etiology of CHDs**

Congenital heart defects account for a significant proportion of all congenital anomalies:

according to various authors, up to 30% of children with any congenital anomalies have

cardiovascular system pathologies [1]. Overall, the global prevalence of CHDs is estimated

at 0.8% to 1.2% per 1,000 live births, although these rates may vary in different regions

[2,3].

Risk factors for CHDs can be divided into genetic, intrauterine (antenatal), and external

(environmental, socio-domestic) factors. The genetic nature of CHDs is supported by the

presence of chromosomal abnormalities (e.g., trisomy 21, 13, 18) and microdeletions


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(22q11.2—DiGeorge syndrome), which significantly increase the risk of heart defects [7].

There are also several monogenic mutations that affect the process of cardiogenesis [6].

Intrauterine factors may include maternal infections during pregnancy (rubella,

cytomegalovirus, toxoplasmosis), maternal diabetes, hormonal dysfunctions, toxic exposures

(alcohol, smoking, drugs), and the use of certain pharmacological agents with teratogenic

potential [16]. The literature also highlights the role of chronic stress and adverse

environmental factors (air pollution, high doses of radiation) [11]. Maternal age over 35

years, especially with a family history of CHDs, is also an important predisposing factor

[7,17].

**Classification of Congenital Heart Defects**

Various classification systems for CHDs are proposed in domestic and foreign literature, but

the most common approach is to categorize defects based on hemodynamic characteristics,

such as defects with increased pulmonary blood flow, decreased pulmonary blood flow,

combined defects, and "cyanotic" and "acyanotic" defects (based on the presence or absence

of cyanosis) [18].

Defects with increased pulmonary blood flow include, for example, ventricular septal

defects (VSD), atrial septal defects (ASD), patent ductus arteriosus (PDA), and other

anomalies associated with left-to-right shunting [26]. "Cyanotic" defects (e.g., tetralogy of

Fallot, transposition of the great arteries) are characterized by cyanosis due to the shunting

of venous blood into the systemic circulation [15]. There are also complex combined defects

involving multiple components (e.g., triads or pentads of Fallot).

Some authors distinguish critical CHDs, where surgical intervention or emergency palliative

measures are necessary for the child's survival (e.g., hypoplastic left heart syndrome, total

anomalous pulmonary venous connection) [21]. This classification has practical significance,

as it determines the urgency of surgical treatment and the need for specialized resuscitation

measures in the delivery room or during the first days of life [27].

**Clinical Manifestations**

The clinical manifestations of congenital heart defects in children vary depending on the

type of defect, the severity of hemodynamic disturbances, and the degree of compensation

[19]. The most severe forms typically manifest immediately after birth or in the first weeks

of life (severe cyanosis, respiratory failure, circulatory disturbances), while milder defects

(e.g., small VSD) may remain asymptomatic for a long time [9,18].

Key symptoms that may suggest CHDs in neonates include:

- Severe dyspnea or cyanotic episodes;

- Cyanosis of the nasolabial triangle, mucous membranes, or skin (especially during crying

or feeding);

- Tachycardia or, conversely, bradycardia;


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- Signs of heart failure (hepatomegaly, edema, poor weight gain);

- Characteristic auscultatory findings (murmurs, accentuated second heart sound over the

pulmonary artery, etc.) [19,20].

In older children, if the defect is non-critical and did not manifest in the neonatal period,

symptoms may include fatigue, dyspnea during physical activity, frequent respiratory

infections, and delayed physical development [8,22].

**Modern Diagnostic Methods**

Standard diagnostic methods for CHDs in pediatric practice include:

1. Clinical examination: history taking (including family history), physical examination,

auscultation, and assessment of skin and mucous membrane color [19].

2. Electrocardiography (ECG): allows for the evaluation of rhythm, conduction, and cardiac

chamber hypertrophy [20].

3. Chest X-ray: provides information on heart size and pulmonary vascular markings [5].

4. Echocardiography with Doppler: the primary method for visualizing cardiac anatomy and

major vessels, detecting septal defects, abnormal blood flows, valve regurgitation, etc. [8,28].

5. Fetal echocardiography: performed prenatally (from 18–20 weeks of gestation) to detect

major CHDs and assess fetal blood flow [10].

6. Cardiac catheterization and angiocardiography: invasive methods used in complex

diagnostic cases and for clarifying hemodynamic parameters before surgical intervention

[20].

7. Genetic testing: indicated in cases of suspected chromosomal abnormalities or hereditary

syndromes associated with CHDs [29].

In recent years, advanced imaging techniques such as cardiac magnetic resonance imaging

(MRI) and multislice computed tomography (CT) with three-dimensional reconstruction

have gained wider use [30]. These methods provide detailed visualization of the defect's

structure and aid in planning surgical interventions.

**Medical Therapy and Palliative Measures**

In most cases, congenital heart defects with significant hemodynamic disturbances require

surgical correction. However, medical therapy is often used in preparation for surgery and to

maintain compensation [31]. Medications of choice include diuretics (furosemide,

spironolactone), inotropic agents (cardiac glycosides), vasodilators (ACE inhibitors), beta-

blockers, and others [32]. In some defects (e.g., PDA) in preterm infants, ibuprofen or

indomethacin may be used to close the ductus arteriosus [33].


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Surgical Treatment

The primary method for radical correction or repair of CHDs is surgical intervention.

Depending on the type of defect, the child's age, and condition, surgeries may be performed

on an emergency, early, or delayed basis [14,21]. The main types of interventions include:

- Radical: completely correcting the anatomical defect (e.g., VSD closure, ASD repair, PDA

ligation).

- Palliative: improving hemodynamics without fully correcting the defect (e.g.,

aortopulmonary anastomosis, shunt creation).

- Single-stage and multi-stage (staged correction): particularly relevant for complex

combined defects (tetralogy of Fallot, transposition of the great arteries, hypoplastic left

heart syndrome) [27].

One of the achievements of modern cardiac surgery is the widespread use of endovascular

(catheter-based) interventions: occluder placement for ASD and VSD, endovascular closure

of PDA, and stenting of narrowed segments (e.g., in coarctation of the aorta) [34]. These

methods are less invasive, reduce hospitalization time, and are highly effective for certain

indications.

Rehabilitation and Long-Term Outcomes

Rehabilitation of children who have undergone surgical treatment for CHDs includes a range

of measures: medical support, hemodynamic monitoring, nutritional and physical activity

adjustments, and psychological and educational assistance [35]. Regular follow-up with a

cardiologist and pediatrician allows for the timely detection of potential complications

(restenosis, arrhythmias, heart failure) and adjustment of therapy [36].

The prognosis for children with CHDs has significantly improved compared to 20–30 years

ago. According to some data, with timely radical surgery, children with the most common

defects (VSD, ASD, PDA) can achieve nearly normal life expectancy [23]. However, for

critical CHDs requiring multi-stage interventions, the risk of complications and mortality

remains high [15,27].

Prevention of Congenital Heart Defects

Prevention of CHDs aims to reduce the risk of defects during the intrauterine period and to

ensure early detection and timely treatment [17,25]. Prenatal counseling for expectant

parents, considering genetic factors, and maintaining a healthy lifestyle during pregnancy

(avoiding alcohol and other teratogenic substances, managing chronic conditions) play a

crucial role [7,16].

In cases of a family history of CHDs or suspected genetic disorders, genetic screening and

high-precision prenatal diagnosis (non-invasive prenatal testing, amniocentesis if necessary)

are recommended [29]. Folic acid supplementation during pregnancy planning is also


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advised, as it not only reduces the risk of neural tube defects but may also positively impact

overall fetal development [37].

Timely ultrasound screening during the first and second trimesters of pregnancy (including

fetal echocardiography) allows for the detection of most severe forms of CHDs and

determines the management strategy for delivery (e.g., delivery in a specialized perinatal

center with the capability for neonatal surgery within the first hours of life) [10,38].

Discussion

The analysis of modern scientific literature highlights the significant impact of congenital

heart defects as one of the leading causes of childhood mortality and disability [3,4].

Advances in medical science and technological progress in perinatal diagnosis and cardiac

surgery have led to substantial improvements: survival rates for severe CHDs have increased,

and early mortality rates have decreased [15,23].

However, according to some authors, challenges remain in the uneven availability of high-

tech care across regions and insufficient prenatal screening coverage [11,25]. Additionally,

organizational issues related to the creation of multidisciplinary teams (obstetricians,

cardiologists, neonatologists, cardiac surgeons) working in close collaboration for timely

diagnosis and treatment of CHDs are crucial [39].

Further research is needed to clarify the genetic mechanisms underlying CHDs, which could

lead to the development of primary prevention methods. Currently, molecular genetic

research aimed at identifying specific genes responsible for cardiogenesis and mutations that

increase the risk of CHDs is actively progressing [6,7].

Long-term follow-up of children with CHDs, including postoperative outcomes, will

provide a better understanding of factors influencing quality and length of life in these

patients. Research on psychosocial aspects is also important, as children with severe defects

may experience psychological difficulties and physical limitations, affecting their

socialization [35,40].

Conclusion

1. Congenital heart defects in children remain a pressing issue in pediatrics and pediatric

cardiac surgery, contributing significantly to childhood mortality and disability.

2. The main risk factors include genetic and chromosomal abnormalities, adverse pregnancy

conditions, teratogenic exposures, and environmental factors.

3. Modern diagnostic methods (prenatal echocardiography, echocardiography with color

Doppler, CT, and MRI of the heart) enable early detection of CHDs and planning of timely

surgical or interventional interventions.

4. Surgical and endovascular interventions allow for the radical correction of many forms of

CHDs; however, long-term rehabilitation and follow-up are necessary.


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5. Prevention of congenital heart defects involves a range of measures—from pregnancy

planning and proper prenatal care to promoting healthy lifestyles and genetic counseling.

The development of a multidisciplinary approach, further advancements in diagnostic and

surgical technologies, and research into the genetic basis of CHDs offer opportunities for

reducing the incidence of CHDs and improving the quality of life for affected children.

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Heart. 2020;106(9):681-686.

40. Исаева ДП, Дроздова ЮС, Бабенко ПВ. Психологическая адаптация детей с

врожденными пороками сердца после оперативного лечения. Вопросы детской

психологии. 2022;15(3):72-78.

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