Authors

  • L. Khaydarova
    Andijan State Medical Institute

DOI:

https://doi.org/10.71337/inlibrary.uz.jmsi.123946

Abstract

The most common forms of congenital heart defects (CHDs) in children include ventricular septal defect (VSD), atrial septal defect (ASD), and Tetralogy of Fallot. The natural course of these defects is often complicated by the development of severe complications caused by arterial hypoxia. The high mortality rate associated with septal heart defects in children is primarily due to progressive congestive heart failure and pulmonary hypertension. In patients with cyanotic CHDs, the leading pathogenetic factor is diffuse hypoxemia. Insufficient arterial blood oxygenation exacerbates the clinical manifestations of the defect and contributes to the development of cardiac arrhythmias, which may be regarded as an additional adverse prognostic factor in congenital heart disease.


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volume 4, issue 5, 2025

1048

UDK 616.124.6-053.2-07-08-036

ARTERIAL HYPOXIA AS A FACTOR AFFECTING THE COURSE OF CONGENITAL

HEART DEFECTS IN CHILDREN

Khaydarova L.R.

Andijan State Medical Institute

Republic of Uzbekistan

Abstract:

The most common forms of congenital heart defects (CHDs) in children include

ventricular septal defect (VSD), atrial septal defect (ASD), and Tetralogy of Fallot. The natural

course of these defects is often complicated by the development of severe complications caused

by arterial hypoxia. The high mortality rate associated with septal heart defects in children is

primarily due to progressive congestive heart failure and pulmonary hypertension. In patients

with cyanotic CHDs, the leading pathogenetic factor is diffuse hypoxemia. Insufficient arterial

blood oxygenation exacerbates the clinical manifestations of the defect and contributes to the

development of cardiac arrhythmias, which may be regarded as an additional adverse prognostic

factor in congenital heart disease.

Keywords:

congenital heart defects, arterial hypoxemia, VSD, ASD, Tetralogy of Fallot, ECG,

cardiac arrhythmias.

Relevance:

Congenital heart defects (CHDs) represent the most prevalent group of

developmental anomalies in children and remain a leading cause of disability and mortality in the

pediatric population [3,4,9]. Moreover, a further increase in the incidence of CHDs is projected.

This trend may be partly attributed to advancements in diagnostic techniques, including

improved training of ultrasound specialists and enhanced imaging technologies [6,7,10].

The prognosis of children with congenital heart defects (CHDs) depends on the type of defect,

the degree of arterial hypoxia, the timeliness of diagnosis, and the presence of comorbid

conditions [3,8].

The most prevalent defects belong to the so-called “big six,” including ventricular septal defect

(VSD), atrial septal defect (ASD), and Tetralogy of Fallot [1,2,7]. The natural progression of

these defects is often associated with the development of severe complications. In children with

acyanotic CHDs, the primary causes of death are congestive heart failure and the development of

pulmonary hypertension. In contrast, children with cyanotic CHDs have a high mortality rate due

to profound hypoxemia and thromboembolic complications [1,3,5].

The key mechanisms underlying impaired cardiac hemodynamics in these defects include

volume or pressure overload of cardiac chambers. Prolonged exposure to these conditions

depletes compensatory mechanisms, leading to chamber dilation and hypertrophy, which

subsequently results in heart failure. Heart failure, in turn, causes systemic hemodynamic

disturbances, contributing to either pulmonary hyperemia or hipoemia. This leads to the clinical

manifestations of circulatory hypoxia—regional in VSD and ASD, and diffuse in Tetralogy of

Fallot [1,5,9,10].

Pulmonary hyperemia (pulmonary hypertension) in VSD and ASD is a significant risk factor for

recurrent pneumonia, while diffuse hypoxia can lead to multiple organ dysfunction. Structural

remodeling of the heart due to dilation and hypertrophy, along with hypoxic, ischemic, and

metabolic disturbances in the myocardium, may contribute to conduction system disorders and

be accompanied by various arrhythmias, which further aggravate the clinical course of CHDs


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[1,4,5].

In this regard, our objective was to study the impact of arterial hypoxia on the course of

congenital heart defects (CHDs) in young children.

Results

: The study and data collection were conducted at the Andijan Regional Multidisciplinary

Children's Center. To address the objectives of this research, we examined children who received

treatment in the Cardiorheumatology Department during the year 2024, along with a

retrospective review of medical records.

The study included 71 children aged from 6 months to 3 years, of whom 72% were between 1

and 3 years old. In terms of gender distribution, boys predominated (55% compared to 45%),

both in the group under 1 year of age and in the older age group.

Based on the hemodynamic patterns of the circulatory system, we selected patients with septal

defects and pulmonary hypertension: specifically, ventricular septal defect (VSD) and atrial

septal defect (ASD). The cyanotic defect included in our study was the complex,

multicomponent Tetralogy of Fallot.

Upon hospital admission, 81,7% of the children were assessed as being in severe condition,

primarily due to symptoms of grade II heart failure. Capillary blood oxygen saturation levels

were measured in all children at the time of admission. The lowest oxygen saturation levels—

ranging from 91% to 84%—were observed in children with Tetralogy of Fallot. In children with

septal defects, the saturation levels were as follows: 94–88% in cases of ventricular septal defect

(VSD) and 93–91% in atrial septal defect (ASD).


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Frequent respiratory infections and repeated hospitalizations were observed in all of the children

included in our study. The results we obtained are consistent with data reported in the literature.

The nature of complaints in all examined children with congenital heart defects (CHDs) was

dependent on the degree of hypoxia. The most common and universal symptom, regardless of the

type of hemodynamic disturbance, was dyspnea, which was recorded in 88,6% of children with

ventricular septal defect (VSD), 77,8% of those with atrial septal defect (ASD), and in all

children with Tetralogy of Fallot. In children with septal defects, the incidence of dyspnea was

associated with excessive pulmonary blood flow, whereas in Tetralogy of Fallot, it was caused

by arterial hypoxemia due to right-to-left shunting.

Hemodynamic disturbances in these heart defects were also reflected in the results of

electrocardiographic (ECG) examinations. Regardless of the degree of arterial hypoxemia,

abnormalities in cardiac automatism were represented by sinus tachycardia and sinus

tachyarrhythmia. Increased electrical activity of the right ventricle was recorded in children with

both ventricular and atrial septal defects.

Conduction disorders of varying frequency were observed in all examined children. Incomplete

right bundle branch block (RBBB) was detected in 80% of children with VSD, 33.3% with ASD,

and 50% with Tetralogy of Fallot. Complete RBBB was found exclusively in children with

Tetralogy of Fallot (5,6%). First-degree atrioventricular (AV) block was registered in three

children (8,6%) with large ventricular septal defects and in one child with Tetralogy of Fallot.

ECG changes in children with VSD (n=35).

ECG sign

Аbs.

%

Sinus tachycardia

26

74,3%

Sinus arrhythmia

9

25,7%

Incomplete right bundle branch block (RBBB)

28

80%

AV block 1 degree

3

8,6%

High electrical activity of the right ventricle

7

20%

Left ventricular hypertrophy

18

51,5%

Right ventricular hypertrophy

17

48,5%

Таbl. 1

ECG changes in children with ASD (n=18).


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ECG sign

Аbs.

%

Sinus tachycardia

18

100%

Incomplete right bundle branch block (RBBB)

6

33,3%

High electrical activity of the right ventricle

9

50%

Right ventricular hypertrophy

11

61,1%

Таbl.2

ECG changes in children with tetralogy of Fallot (n=18).

ECG sign

Аbs.

%

Sinus tachycardia

3

16,7%

Sinus tachyarrhythmia

8

44,4%

Incomplete right bundle branch block

9

50%

Complete right bundle branch block

1

5,6%

AV block 1 degree

1

5,6%

Right ventricular hypertrophy

18

100%

Таbl. 3

Electrocardiographic signs of right ventricular hypertrophy were observed in 48,5% of children

with ventricular septal defect (VSD), 61,1% of those with atrial septal defect (ASD), and in all

children with Tetralogy of Fallot. Signs of left ventricular hypertrophy were noted in 51,5% of

children with VSD.

Structural changes in heart chambers and the dimensions of congenital defects were assessed

based on echocardiography findings. Among children with VSD (35 cases), the largest

proportion had defects measuring 4–8 mm (48,6%), followed by those with defects ≤4 mm

(34,3%), and defects >8 mm in 17,1% of cases. For ASD (18 children), the distribution by defect

size was as follows: up to 5 mm – 61,1% of cases, and 6–10 mm – 38,9%.

Among children with Tetralogy of Fallot, 66,7% had a ventricular septal defect measuring 6–10

mm, while the remaining children had defects larger than 10 mm. Regarding the localization of

right ventricular outflow tract obstruction, 72,2% had narrowing in the infundibular region, while

in 27,8% the stenosis was located at the level of the pulmonary valve.

Pulmonary hypertension in children with septal defects manifested on chest radiography as an

enhanced pulmonary vascular pattern along the arterial branches. In contrast, in Tetralogy of

Fallot, increased pulmonary translucency was due to a reduced vascular pattern. Cardiomegaly

was identified in all examined children—74,6% due to right ventricular enlargement, and 25,4%

due to left ventricular enlargement, the latter observed exclusively in children with VSD.

Thus, we established a correlation between arterial hypoxia and both the course and severity of

clinical manifestations of CHDs. The lower the oxygen saturation in arterial blood, the more

severe the clinical symptoms and the more pronounced the cardiac rhythm disturbances, which

may serve as an additional prognostic risk factor in congenital heart defects.

Sources used:

1. K.T. Bayakova, B.Zh. Zhumazhanova i dr. Vrozhdennye poroki serdtsa: Tetrada Fallo

(klinicheskiy sluchay). // Zhurnal kazakhstansko-rossiyskogo meditsinskogo universiteta

«Aktual'nye problemy teoreticheskoy i klinicheskoy meditsiny», №3 (37) 2022, pp.34–40.

2. Bokeriya L.A., Kim A.I. i dr. Defekt mezhpredserdnoy peregorodki. Klinicheskie

rekomendatsii 2023. // Rossiyskiy kardiologicheskiy zhurnal, tom 28, №8, 2023.


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3. Efimenko O.V., Khaydarova L.R. i dr. Vliyanie arterial'noy gipoksii na techenie

vrozhdennykh porokov serdtsa u detey rannego vozrasta. Ekonomika i sotsium, 2021, №4

(83),pp.1101–1106.

4. Efimenko O.V., Khaydarova L.R. Vliyanie gemodinamicheskikh rasstroystv na kachestvo

zhizni detey s vrozhdennymi porokami serdtsa. Ekonomika i sotsium, 2023, №4 (107), pp.560–

565.

5. Efimenko O.V., Khaydarova L.R. Gemodinamicheskie narusheniya i prognoz u detey s ne

korragirovannym defektom mezhzheludochkovoy peregorodki. // Vestnik Tashkentskoy

meditsinskoy akademii, 2024, spets. vypusk, tom 2, pp.15–18.

6. Kalashnikova E.A., Nikitina N.A. Rannyaya neontal'naya, postnatal'naya diagnostika,

klinicheskaya manifestatsiya, lechenie i prognoz pri defekte mezhzheludochkovoy peregorodki.

Na dopomogu pediatru / 2016, №6 (74), pp.63–67.

7. Kalashnikova E.A., Nikitina N.A. Defekt mezhzheludochkovoy peregorodki: osobennosti

rannoy neontal'noy i postnatal'noy diagnostiki, klinicheskoy manifestatsii, lecheniya i prognoza

na sovremennom etape. Na dopomogu pediatru / Ty Help the Pediatrician / 2016, №4 (72),

pp.71–75.

8. Saperova E.V., Vakhlova I.V. Kompleksnaya otsenka sostoyaniya zdorovya detey pervogo

goda zhizni s DMJP. Meditsinskiy sovet, 2017, №19, pp.198–204.

9. Saperova E.V., Vakhlova I.V. Vrozhdyonnye poroki serdtsa u detey: rasprostronennost',

faktory riska, smertnost'. Voprosy sovremennoy pediatrii, 2017, tom 16, №2, pp.126–133.

10. Efimenko O.V., Khaydarova L.R. Clinical and instrumental assessment of the current

congenital heart defect in early age children depending on the severity of arterial hypoxia.

Ekonomika i sotsium, 2022, №2 (93), pp.42–51.

References

K.T. Bayakova, B.Zh. Zhumazhanova i dr. Vrozhdennye poroki serdtsa: Tetrada Fallo (klinicheskiy sluchay). // Zhurnal kazakhstansko-rossiyskogo meditsinskogo universiteta «Aktual'nye problemy teoreticheskoy i klinicheskoy meditsiny», №3 (37) 2022, pp.34–40.

Bokeriya L.A., Kim A.I. i dr. Defekt mezhpredserdnoy peregorodki. Klinicheskie rekomendatsii 2023. // Rossiyskiy kardiologicheskiy zhurnal, tom 28, №8, 2023.

Efimenko O.V., Khaydarova L.R. i dr. Vliyanie arterial'noy gipoksii na techenie vrozhdennykh porokov serdtsa u detey rannego vozrasta. Ekonomika i sotsium, 2021, №4 (83),pp.1101–1106.

Efimenko O.V., Khaydarova L.R. Vliyanie gemodinamicheskikh rasstroystv na kachestvo zhizni detey s vrozhdennymi porokami serdtsa. Ekonomika i sotsium, 2023, №4 (107), pp.560–565.

Efimenko O.V., Khaydarova L.R. Gemodinamicheskie narusheniya i prognoz u detey s ne korragirovannym defektom mezhzheludochkovoy peregorodki. // Vestnik Tashkentskoy meditsinskoy akademii, 2024, spets. vypusk, tom 2, pp.15–18.

Kalashnikova E.A., Nikitina N.A. Rannyaya neontal'naya, postnatal'naya diagnostika, klinicheskaya manifestatsiya, lechenie i prognoz pri defekte mezhzheludochkovoy peregorodki. Na dopomogu pediatru / 2016, №6 (74), pp.63–67.

Kalashnikova E.A., Nikitina N.A. Defekt mezhzheludochkovoy peregorodki: osobennosti rannoy neontal'noy i postnatal'noy diagnostiki, klinicheskoy manifestatsii, lecheniya i prognoza na sovremennom etape. Na dopomogu pediatru / Ty Help the Pediatrician / 2016, №4 (72), pp.71–75.

Saperova E.V., Vakhlova I.V. Kompleksnaya otsenka sostoyaniya zdorovya detey pervogo goda zhizni s DMJP. Meditsinskiy sovet, 2017, №19, pp.198–204.

Saperova E.V., Vakhlova I.V. Vrozhdyonnye poroki serdtsa u detey: rasprostronennost', faktory riska, smertnost'. Voprosy sovremennoy pediatrii, 2017, tom 16, №2, pp.126–133.

Efimenko O.V., Khaydarova L.R. Clinical and instrumental assessment of the current congenital heart defect in early age children depending on the severity of arterial hypoxia. Ekonomika i sotsium, 2022, №2 (93), pp.42–51.